Complete Information on Cutis laxa

Cutis laxa too called elastolysis. It is a group of uncommon connective tissue disorders in which the rind becomes inelastic and hangs broadly in folds. Cutis laxa can be balmy, affecting simply an individual's show, or serious, affecting the domestic organs. It is characterized by rind that is lax (weak), hanging, wrinkled, and lacking in elasticity (hyperelasticity. The stricken areas of rind may be thickened and blue. The disorder involves a kind of symptoms and signs that ensue from defects in connective tissue.

Defective connective tissue may induce problems in the vocal cords, bones, cartilage, blood vessels, bladder, kidney, digestive structure, and lungs. In most cases, cutis laxa is inherited. Cutis Laxa can be autosomal recessive, autosomal predominant or X-linked. In some kinds of cutis laxa, the irregular genes induce problems unconnected to connective tissues. Congenital forms of CL are more popular than acquired disease. The recessively inherited kind is almost regular and almost serious. Approximately one half of the cases of acquired CL are associated with a preceding incendiary outbreak.

CL affects persons of all races. CL affects men and women evenly. Treatment of cutis laxa largely pastic operation. Plastic operation can frequently better the show of the rind, although the advance may be simply short-lived. Severe impairments of the eye, lungs, arteries, or intestines can be deadly. Botulinum toxin injections are being considered for improving the aged show and facial defects seen in persons with CL. Cosmetic surgery to reduce redundant skin folds may be performed but often produces only temporary benefit. Patients with cutis laxa, particularly those with the autosomal dominant form usually have a normal life expectancy.